Clinical Aspects of Congenital Hepatic Fibrosis

Hepatomegaly	
Portal hypertension 	
Splenomegaly/hypersplenism	
Renal disease:	infantile polycystic disease with progressive renal failure
                          	palpable kidneys
                          	asymptomatic disease
                          	nepronophthisis          	
Cholangitis	
Cholestasis/jaundice	
Intrahepatic stone formation	
Intrahepatic cystic dilatation	
Extrahepatic cystic dilatation	
Hepatocellular or cholangiolar carcinoma	
Hepatic failure